Recombinant Glucosamine (N-acetyl) -6-Sulfatase/G6S Monoclonal Antibody
Product Specifications
Background
The product of this gene is a lysosomal enzyme found in all cells. It is involved in the catabolism of heparin, heparan sulphate, and keratan sulphate. Deficiency of this enzyme results in the accumulation of undegraded substrate and the lysosomal storage disorder mucopolysaccharidosis type IIID (Sanfilippo D syndrome) . Mucopolysaccharidosis type IIID is the least common of the four subtypes of Sanfilippo syndrome.
Abbreviation
GNS
UniProt
P15586
Host
Rabbit
Reactivity
Human
Immunogen
Recombinant Human GNS protein
Target
GNS; G6S; Glucosamine-6-Sulfatase; N-Acetylglucosamine-6-Sulfatase
Clonality
Monoclonal
Clone
4D5
Conjugation
Unconjugated
Applications
WB
Field of Research
Tags & Cell Markers; Signal Transduction; Cell Biology; Metabolism
Purification
Protein A
Concentration
1 mg/mL
Dilution
WB 1:500-1:2000
Buffer
0.2 μm filtered solution in PBS
Shipping Conditions
Ice bag
Storage Conditions
This antibody can be stored at 2°C-8°C for one month without detectable loss of activity. Antibody products are stable for twelve months from date of receipt when stored at -20°C to -80°C. Preservative-Free. Avoid repeated freeze-thaw cycles.
Product Datasheet
https://789.bio/ea/mwffha8u
Product MSDS
https://789.bio/eb/g6amDTwb
Calculated Molecular Weight
62 kDa
Observed Molecular Weight
95 kDa
Isotype
IgG
Curated Selection
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