Galactosidase alpha Rabbit Polyclonal Antibody
This gene encodes a homodimeric glycoprotein that hydrolyses the terminal alpha-galactosyl moieties from glycolipids and glycoproteins. This enzyme predominantly hydrolyzes ceramide trihexoside, and it can catalyze the hydrolysis of melibiose into galactose and glucose. A variety of mutations in this gene affect the synthesis, processing, and stability of this enzyme, which causes Fabry disease, a rare lysosomal storage disorder that results from a failure to catabolize alpha-D-galactosyl glycolipid moieties.
Product Specifications
CAS Number
9007-83-4
Product Name Alternative
Abbreviation
GLA
Swiss Prot
P06280 Human
Cellular Locus
Lysosome.
Host
Rabbit
Species Reactivity
Human
Immunogen
Recombinant protein within human Galactosidase alpha aa 81-280.
Isotype
IgG
Conjugation
Non-conjugated
Type
Rabbit polyclonal Antibody
Applications
WB, IF-Cell, IHC-P
Positive Control
293T cell lysate, MCF-7 cell lysate, Hela, human breast tissue, human endometrium tissue, human kidney tissue.
Concentration
1 mg/mL
Dilution
WB: 1:500;IF-Cell: 1:200;IHC-P: 1:600
Purity
Immunogen affinity purified.
Form
Liquid
Buffer
PBS (pH7.4), 0.05% BSA, 40% Glycerol. Preservative: 0.05% Sodium Azide.
Molecular Weight
Predicted band size: 49 kDa
Storage Conditions
Store at +4°C after thawing. Aliquot store at -20°C. Avoid repeated freeze/thaw cycles.
Recombinant Antibody
No
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