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OPA1 Polyclonal Antibody

Product Specifications

Background

This gene product is a nuclear-encoded mitochondrial protein with similarity to dynamin-related GTPases. It is a component of the mitochondrial network. Mutations in this gene have been associated with optic atrophy type 1, which is a dominantly inherited optic neuropathy resulting in progressive loss of visual acuity, leading in many cases to legal blindness. Multiple transcript variants encoding different isoforms have been found for this gene.

CAS Number

9007-83-4

Synonyms

Dynamin-like 120 kDa protein, mitochondrial ;Optic atrophy protein 1 [Cleaved into: Dynamin-like 120 kDa protein, form S1]

Host

Rabbit

Reactivity

Human, Mouse, Rat

Immunogen

Synthesized peptide derived from part region of human protein

Clonality

Polyclonal

Applications

WB, ELISA

Stability

-20°C for 1 year

Concentration

1 mg/ml

Antibody Type

Primary antibody

Isotype

IgG

Available Sizes

Frequently Asked Questions

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