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FXN Recombinant Rabbit mAb

Product Specifications

Background

This nuclear gene encodes a mitochondrial protein which belongs to the FRATAXIN family. The protein functions in regulating mitochondrial iron transport and respiration. The expansion of intronic trinucleotide repeat GAA from 8-33 repeats to >90 repeats results in Friedreich ataxia. Alternative splicing results in multiple transcript variants. [provided by RefSeq, Jul 2016]

CAS Number

9000-83-3

Structure Composition

Store at -20°C. Supplied in 50mM Tris-Glycine (pH 7.4), 0.15M NaCl, 40%Glycerol, 0.01% sodium azide and 0.05% BSA. Stable for 12 months from date of receipt.

Product Name Alternative

FA; X25; CyaY; FARR; FRDA

Swiss Prot

Q16595, O35943, D3ZYW7

Reactivity

Human, Mouse, Rat

Immunogen

Recombinant protein of human FXN

Conjugation

Unconjugated

Applications

WB, IHC, ICC/IF, FC, IP

Purity

Affinity Purification

Modification

Unmodification

Molecular Weight

14 kDa

Storage Conditions

Store at 4°C short term. Aliquot and store at -20°C long term. Avoid freeze-thaw cycles.

Notes

For research use only, not for use in diagnostic procedure.

Specificity

IgG

Applications Notes

Western blot analysis of extracts from Rat kidney tissue using BS49349 at 1: 1000.

Host or Source

Rabbit

Available Sizes

Curated Selection

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