FKRP polyclonal antibody
Product Specifications
Background
This gene encodes a protein which is targeted to the medial Golgi apparatus and is necessary for posttranslational modification of dystroglycan. Mutations in this gene have been associated with congenital muscular dystrophy, mental retardation, and cerebellar cysts. Several alternatively spliced transcript variants of this gene have been described, but the full-length nature of some of these variants has not been determined. [provided by RefSeq, Oct 2008]
CAS Number
9007-83-4
Structure Composition
Rabbit IgG, 1mg/ml in PBS with 0.02% sodium azide, 50% glycerol, pH7.2
Product Name Alternative
Fukutin-related protein
Swiss Prot
Q9H9S5
Reactivity
Human
Immunogen
Recombinant protein of human FKRP.
Conjugation
Unconjugated
Applications
WB, IHC
Dilution
WB 1:2000 - 1:5000 IHC 1:50 - 1:200
Purity
The antibody was affinity-purified from rabbit antiserum by affinity-chromatography using epitope-specific immunogen and the purity is > 95% (by SDS-PAGE) .
Modification
Unmodification
Molecular Weight
~ 45 kDa
Storage Conditions
Store at 4°C short term. Aliquot and store at -20°C long term. Avoid freeze-thaw cycles.
Notes
For research use only, not for use in diagnostic procedure.
Specificity
FKRP polyclonal antibody detects endogenous levels of FKRP protein.
Applications Notes
Western blot analysis of extracts of various cells, using FKRP antibody.
Host or Source
Rabbit
Available Sizes
Frequently Asked Questions
More Discoveries
Explore Other Products
Browse additional items from our catalog
LC424921 20 µg
Cytochrome P450 2D6 (CYP2D6) (NM_000106) Human Over-expression Lysate
Sign In for Pricing
View Details 
RDR-PDIA6-Hu-01 96 Tests
Human Protein Disulfide Isomerase A6 (PDIA6) ELISA Kit
Sign In for Pricing
View Details RDR-PDIA6-Hu-02 48 Tests
Human Protein Disulfide Isomerase A6 (PDIA6) ELISA Kit
Sign In for Pricing
View Details 