GBA Rabbit monoclonal antibody
Product Specifications
Background
Defects in GBA are the cause of Gaucher disease (GD) [MIM:230800]; also known as glucocerebrosidase deficiency. GD is the most prevalent lysosomal storage disease, characterized by accumulation of glucosylceramide in the reticulo-endothelial system.
CAS Number
9007-83-4
Structure Composition
Rabbit IgG, 1mg/ml in PBS with 0.02% sodium azide, 50% glycerol, pH7.2.
Product Name Alternative
Alglucerase; betaGC; GBA1; GCase; GCB; GLUC; Glucosylceramidase; Imiglucerase
Swiss Prot
P04062
Reactivity
Human Rat
Immunogen
A synthesized peptide derived from human GBA
Conjugation
Unconjugated
Applications
WB IHC
Dilution
WB 1:500~1:2000 IHC 1:50~1:200
Purity
Affinity-chromatography
Modification
Unmodified
Molecular Weight
60kDa
Storage Conditions
Store at 4°C short term. Aliquot and store at -20°C long term. Avoid freeze-thaw cycles.
Notes
For research use only, not for use in diagnostic procedure.
Specificity
GBA Antibody detects endogenous levels of total GBA
Applications Notes
Western blot analysis of GBA expression in U87-MG cell lysate.
Host or Source
Rabbit
Available Sizes
Curated Selection
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