L-2-Aminobutyric acid
L-2-Aminobutyric acid, one of the three isomers of aminobutyric acid, is elevated in the plasma of children with with Reye's syndrome, tyrosinemia, homocystinuria, nonketotic hyperglycinemia, and ornithine transcarbamylase deficiency.
Product Specifications
CAS Number
[1492-24-6]
Product Name Alternative
H-Abu-OH
UNSPSC
12352211
Hazard Statement
H302, H315, H319, H335
Target
Endogenous Metabolite
Type
Natural Products
Related Pathways
Metabolic Enzyme/Protease
Applications
Metabolism-protein/nucleotide metabolism
Field of Research
Metabolic Disease
Assay Protocol
https://www.medchemexpress.com/H-Abu-OH.html
Purity
99.39
Solubility
H2O : 50 mg/mL (ultrasonic)
Smiles
CC[C@H](N)C(O)=O
Molecular Formula
C4H9NO2
Molecular Weight
103.12
Precautions
H302, H315, H319, H335
References & Citations
[1]Yudkoff M, et al. On the clinical significance of the plasma alpha-amino-n-butyric acid:leucine ratio. Am J Clin Nutr. 1979 Feb;32 (2) :282-5.
Shipping Conditions
Room Temperature
Storage Conditions
Store at room temperature 3 years
Scientific Category
Natural Products
Clinical Information
No Development Reported
Isoform
Human Endogenous Metabolite
Available Sizes
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