L-Homocitrulline
L-Homocitrulline is metabolized to homoarginine through homoargininosuccinate via the urea cycle pathway and its metabolic abnormality could lead to Lysinuric Protein Intolerance (LPI) .
Product Specifications
CAS Number
[1190-49-4]
UNSPSC
12352211
Hazard Statement
H302, H315, H319, H335
Target
Endogenous Metabolite
Type
Natural Products
Related Pathways
Metabolic Enzyme/Protease
Applications
Metabolism-protein/nucleotide metabolism
Field of Research
Metabolic Disease
Assay Protocol
https://www.medchemexpress.com/L-Homocitrulline.html
Concentration
10mM
Purity
99.53
Solubility
H2O : 33.33 mg/mL (ultrasonic; warming; heat to 60°C)
Smiles
[H][C@](N)(CCCCNC(N)=O)C(O)=O
Molecular Formula
C7H15N3O3
Molecular Weight
189.21
Precautions
H302, H315, H319, H335
References & Citations
[1]Kato T, et al. Homocitrullinuria and homoargininuria in lysinuric protein intolerance. J Inherit Metab Dis. 1989;12 (2) :157-61.
Shipping Conditions
Room Temperature
Storage Conditions
-20°C, 3 years; 4°C, 2 years (Powder)
Scientific Category
Natural Products
Clinical Information
No Development Reported
Available Sizes
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