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L-Homocitrulline

Product Specifications

UNSPSC Description

L-Homocitrulline is metabolized to homoarginine through homoargininosuccinate via the urea cycle pathway and its metabolic abnormality could lead to Lysinuric Protein Intolerance (LPI).

Target Antigen

Endogenous Metabolite

Type

Natural Products

Related Pathways

Metabolic Enzyme/Protease

Applications

Metabolism-protein/nucleotide metabolism

Field of Research

Metabolic Disease

Assay Protocol

https://www.medchemexpress.com/L-Homocitrulline.html

Purity

97.0

Solubility

DMSO : < 1 mg/mL (ultrasonic;warming;heat to 60°C)|H2O : 33.33 mg/mL (ultrasonic;warming;heat to 60°C)

Smiles

[H][C@](N)(CCCCNC(N)=O)C(O)=O

Molecular Weight

189.21

References & Citations

[1]Kato T, et al. Homocitrullinuria and homoargininuria in lysinuric protein intolerance. J Inherit Metab Dis. 1989;12(2):157-61.

Shipping Conditions

Room Temperature

Storage Conditions

-20°C, 3 years; 4°C, 2 years (Powder)

Product Datasheet

http://file.medchemexpress.com/batch_PDF/HY-W018004/L-Homocitrulline-DataSheet-MedChemExpress.pdf

Product MSDS

http://file.medchemexpress.com/batch_PDF/HY-W018004/L-Homocitrulline-SDS-MedChemExpress.pdf

Clinical Information

No Development Reported

CAS Number

1190-49-4

Available Sizes

Curated Selection

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