FH/Fumarase Rabbit pAb
Fumarase (FH) is an enzyme that catalyzes the reversible hydration/dehydration of fumarate to malate in the mitochondria. Fumarase deficiency is caused by a mutation in the fumarase gene in humans. Fumarase deficiency is one of the few known deficiencies of the Krebs cycle or tricarboxylic acid cycle, the main enzymatic pathway of cellular aerobic respiration.
Product Specifications
Background
Product Name Alternative
Fumarase, fumarate hydratase, HLRCC, LRCC, MCL, MCUL1
UniProt
P07954
Swiss Prot
P07954
Reactivity
Human, Rat, Mouse
Immunogen
Recombinant Protein
Clonality
Polyclonal
Source
Rabbit
Applications
WB, IF
Concentration
1mg/mL
Dilution
WB 1:1,000
Buffer
PBS with 0.02% sodium azide and 50% glycerol pH 7.4. Store at -20°C. Avoid repeated freeze-thaw cycles.
Molecular Weight
50kDa
Storage Conditions
PBS with 0.02% sodium azide and 50% glycerol pH 7.4. Store at -20°C. Avoid repeated freeze-thaw cycles.
Observed Molecular Weight
50kDa
Fragment
IgG
Other Product Names
Fumarase, fumarate hydratase, HLRCC, LRCC, MCL, MCUL1
Gene ID (Human)
2271
Available Sizes
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