FH/Fumarase Rabbit pAb
Fumarase (FH) is an enzyme that catalyzes the reversible hydration/dehydration of fumarate to malate in the mitochondria. Fumarase deficiency is caused by a mutation in the fumarase gene in humans. Fumarase deficiency is one of the few known deficiencies of the Krebs cycle or tricarboxylic acid cycle, the main enzymatic pathway of cellular aerobic respiration.
Product Specifications
Background
Synonyms
Fumarase, fumarate hydratase, HLRCC, LRCC, MCL, MCUL1
Gene ID
2271
UniProt
P07954
Host
Rabbit
Species Reactivity
Human,Rat,Mouse
Reactivity
Human, Rat, Mouse
Immunogen
Recombinant Protein
Clonality
Polyclonal
Isotype
IgG
Source
Rabbit
Applications
WB, IF
Validated Applications
WB,IF
Stability
PBS with 0.02% sodium azide and 50% glycerol pH 7.4. Store at -20°C. Avoid repeated freeze-thaw cycles.
Concentration
1 mg/mL
Dilution
WB 1:1,000
Molecular Weight
50kDa
Storage Conditions
PBS with 0.02% sodium azide and 50% glycerol pH 7.4. Store at -20°C. Avoid repeated freeze-thaw cycles.
Product Datasheet
https://www.elkbiotech.com/upload/file/Antibodies/pAb/EA022-1.pdf
Observed Molecular Weight
50 kDa
Other Product Names
Fumarase, fumarate hydratase, HLRCC, LRCC, MCL, MCUL1
Gene ID (Human)
2271
SwissProt (Human)
P07954
Available Sizes
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