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2-Methylbutyrylcarnitine

2-Methylbutyrylcarnitine is a fatty acid metabolite. 2-Methylbutyrylcarnitine is found mainly in the blood and urine of humans and animals and is produced through the pyruvate carboxylation pathway. 2-Methylbutyrylcarnitine exhibits high level in the plasma of subjects with steatohepatitis (NASH) and can be used as an indicator for the diagnosis of metabolic diseases[1].

Product Specifications

CAS Number

[256928-75-3]

UNSPSC

12352211

Hazard Statement

H302, H315, H319, H335

Target

Endogenous Metabolite

Type

Reference compound

Related Pathways

Metabolic Enzyme/Protease

Applications

Metabolism-sugar/lipid metabolism

Field of Research

Metabolic Disease

Assay Protocol

https://www.medchemexpress.com/2-methylbutyrylcarnitine.html

Concentration

10mM

Purity

99.83

Solubility

DMSO : 100 mg/mL (ultrasonic) |H2O : 125 mg/mL (ultrasonic; warming; heat to 60°C)

Smiles

CCC(C)C(O[C@H](CC([O-])=O)C[N+](C)(C)C)=O

Molecular Formula

C12H23NO4

Molecular Weight

245.32

Precautions

H302, H315, H319, H335

References & Citations

[1]Kalhan SC, et al. Plasma metabolomic profile in nonalcoholic fatty liver disease. Metabolism. 2011 Mar;60 (3) :404-13.

Shipping Conditions

Room Temperature

Storage Conditions

-20°C, 3 years; 4°C, 2 years (Powder)

Scientific Category

Reference compound1

Clinical Information

No Development Reported

Available Sizes

Curated Selection

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