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(S) -3,4-Dihydroxybutyric acid (lithium hydrate)

(S) -3,4-Dihydroxybutyric acid (lithium hydrate) is a normal human urinary metabolite that is excreted in increased concentration in patients with succinic semialdehyde dehydrogenase (SSADH) deficiency[1].

Product Specifications

UNSPSC

12352211

Hazard Statement

H302, H312, H332

Target

Endogenous Metabolite

Type

Reference compound

Related Pathways

Metabolic Enzyme/Protease

Applications

Metabolism-protein/nucleotide metabolism

Field of Research

Metabolic Disease

Assay Protocol

https://www.medchemexpress.com/s-3-4-dihydroxybutyric-acid-lithium-hydrate.html

Purity

98.1

Solubility

H2O : 125 mg/mL (ultrasonic)

Smiles

O=C([O-])C[C@H](O)CO.[Li+].[x].[y].O

Molecular Formula

C4H9LiO5

Molecular Weight

144.05

Precautions

H302, H312, H332

References & Citations

[1]Shinka T, et al. Rapid and sensitive detection of urinary 4-hydroxybutyric acid and its related compounds by gas chromatography-mass spectrometry in a patient with succinic semialdehyde dehydrogenase deficiency. J Chromatogr B Analyt Technol Biomed Life Sci. 2002 Aug 25;776 (1) :57-63.

Shipping Conditions

Room Temperature

Storage Conditions

4°C (Powder, sealed storage, away from moisture)

Scientific Category

Reference compound1

Clinical Information

No Development Reported

Isoform

Human Endogenous Metabolite; Microbial Metabolite

Available Sizes

Curated Selection

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