L-Homocitrulline (Standard)

L-Homocitrulline is metabolized to homoarginine through homoargininosuccinate via the urea cycle pathway and its metabolic abnormality could lead to Lysinuric Protein Intolerance (LPI) .

Product Specifications

CAS Number

[1190-49-4]

UNSPSC

12352211

Hazard Statement

H302, H315, H319, H335

Target

Endogenous Metabolite

Related Pathways

Metabolic Enzyme/Protease

Field of Research

Metabolic Disease

Purity

99.96

Smiles

[H][C@](N)(CCCCNC(N)=O)C(O)=O

Molecular Formula

C7H15N3O3

Molecular Weight

189.21

Precautions

H302, H315, H319, H335

References & Citations

[1]Kato T, et al. Homocitrullinuria and homoargininuria in lysinuric protein intolerance. J Inherit Metab Dis. 1989;12 (2) :157-61.

Shipping Conditions

Blue Ice

Storage Conditions

-20°C, sealed storage, away from light and moisture

Scientific Category

Reference Standards

Available Sizes

Curated Selection

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