2-Hydroxy-2-methylbutanoic acid (Standard)

2-Hydroxy-2-methylbutanoic acid (Standard) is the analytical standard of 2-Hydroxy-2-methylbutanoic acid. This product is intended for research and analytical applications. 2-Hydroxy-2-methylbutanoic acid, an unusual metabolite, is associated with 2-hydroxyglutaric aciduria and maple syrup urine disease.

Product Specifications

CAS Number

[3739-30-8]

UNSPSC

12352211

Target

Endogenous Metabolite; Reference Standards

Related Pathways

Metabolic Enzyme/Protease; Others

Field of Research

Metabolic Disease

Smiles

CCC(C)(O)C(O)=O

Molecular Formula

C5H10O3

Molecular Weight

118.13

References & Citations

[1]Dekant W, et al. Biotransformation of MTBE, ETBE, and TAME after inhalation or ingestion in rats and humans. Res Rep Health Eff Inst. 2001 May; (102) :29-71; discussion 95-109.