2-Methylsuccinic acid (Standard)

2-Methylsuccinic acid (Standard) is the analytical standard of 2-Methylsuccinic acid. This product is intended for research and analytical applications. 2-Methylsuccinic acid is a normal metabolite in human fluids and the main biochemical measurable features in ethylmalonic encephalopathy.

Product Specifications

CAS Number

[498-21-5]

Product Name Alternative

Pyrotartaric acid (Standard)

UNSPSC

12352211

Target

Endogenous Metabolite; Reference Standards

Related Pathways

Metabolic Enzyme/Protease; Others

Field of Research

Metabolic Disease

Smiles

O=C(O)C(C)CC(O)=O

Molecular Formula

C5H8O4

Molecular Weight

132.12

References & Citations

[1]Grosso S, et al. Ethylmalonic encephalopathy: further clinical and neuroradiological characterization. J Neurol. 2002 Oct;249 (10) :1446-50.|[2]Nowaczyk MJ, et al. Ethylmalonic and methylsuccinic aciduria in ethylmalonic encephalopathy arise from abnormal isoleucine metabolism. Metabolism. 1998 Jul;47 (7) :836-9.