2-Methylsuccinic acid (Standard)
2-Methylsuccinic acid (Standard) is the analytical standard of 2-Methylsuccinic acid. This product is intended for research and analytical applications. 2-Methylsuccinic acid is a normal metabolite in human fluids and the main biochemical measurable features in ethylmalonic encephalopathy.
Product Specifications
CAS Number
[498-21-5]
Product Name Alternative
Pyrotartaric acid (Standard)
UNSPSC
12352211
Target
Endogenous Metabolite; Reference Standards
Related Pathways
Metabolic Enzyme/Protease; Others
Field of Research
Metabolic Disease
Smiles
O=C(O)C(C)CC(O)=O
Molecular Formula
C5H8O4
Molecular Weight
132.12
References & Citations
[1]Grosso S, et al. Ethylmalonic encephalopathy: further clinical and neuroradiological characterization. J Neurol. 2002 Oct;249 (10) :1446-50.|[2]Nowaczyk MJ, et al. Ethylmalonic and methylsuccinic aciduria in ethylmalonic encephalopathy arise from abnormal isoleucine metabolism. Metabolism. 1998 Jul;47 (7) :836-9.
Shipping Conditions
Room temperature
Scientific Category
Reference Standards
Available Sizes
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