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α-L-Iduronidase

α-L-Iduronidase is key in the catabolism of glycosaminoglycans (GAG) heparan and dermatan sulfate. Measurement of α-L-iduronidase specific enzyme activity is an essential parameter for those studying mucopolysaccharidoses (MPS) type I[1].

Product Specifications

UNSPSC

12352211

Target

Endogenous Metabolite

Related Pathways

Metabolic Enzyme/Protease

Field of Research

Metabolic Disease

Smiles

[a-L-Iduronidase]

References & Citations

[1]Ou L, et al. Standardization of α-L-iduronidase enzyme assay with Michaelis-Menten kinetics. Mol Genet Metab. 2014 Feb;111 (2) :113-5.

Shipping Conditions

Room temperature

Scientific Category

Enzyme

Clinical Information

No Development Reported

Curated Selection

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