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Miglustat (Standard)

Miglustat (Standard) is the analytical standard of Miglustat. This product is intended for research and analytical applications. Miglustat (N-Butyldeoxynojirimycin) is an orally active and reversible ceramide glucosyltransferase inhibitor. Miglustat can be used for the research of type I gaucher disease[1].

Product Specifications

CAS Number

[72599-27-0]

UNSPSC

12352100

Target

Glucosylceramide Synthase (GCS) ; Reference Standards

Related Pathways

Neuronal Signaling; Others

Field of Research

Inflammation/Immunology; Neurological Disease

Smiles

O[C@H]1[C@H](O)[C@@H](CO)N(CCCC)C[C@@H]1O

Molecular Formula

C10H21NO4

Molecular Weight

219.28

References & Citations

[1]Maria Cristina Dechecchi, et al. Anti-inflammatory effect of miglustat in bronchial epithelial cells. J Cyst Fibros. 2008 Nov;7 (6) :555-65. |[2]G D'Arcangelo, et al. Miglustat Reverts the Impairment of Synaptic Plasticity in a Mouse Model of NPC Disease. Neural Plast. 2016:2016:3830424.

Shipping Conditions

Room temperature

Scientific Category

Reference Standards

Available Sizes

Curated Selection

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