Cis-Malonylcarnitine (lithium)
Cis-Malonylcarnitine lithium is an ester compound and a metabolite of Malonyl CoA. The level of cis-Malonylcarnitine lithium is closely related to some diseases, such as malonic aciduria, non-syndromic cleft lip with or without cleft palate, etc[1][2].
Product Specifications
UNSPSC
12352211
Target
Drug Metabolite
Related Pathways
Metabolic Enzyme/Protease
Applications
Metabolism-protein/nucleotide metabolism
Field of Research
Others
Purity
98.3
Smiles
C[N+](C)(C[C@H](OC(CC(O[Li])=O)=O)CC([O-])=O)C
Molecular Formula
C10H16LiNO6
Molecular Weight
253.18
References & Citations
[1]Santer R, et al. Tandem mass spectrometric determination of malonylcarnitine: diagnosis and neonatal screening of malonyl-CoA decarboxylase deficiency. Clin Chem. 2003 Apr;49 (4) :660-2.|[2]Hozyasz KK, et al. Malonylcarnitine in newborns with non-syndromic cleft lip with or without cleft palate. Int J Oral Sci. 2010 Sep;2 (3) :136-41.
Shipping Conditions
Blue Ice
Storage Conditions
-20°C (Powder, sealed storage, away from moisture)
Scientific Category
Natural Products
Clinical Information
No Development Reported
Available Sizes
Frequently Asked Questions
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