Glutarylcarnitine (Standard)
Glutarylcarnitine (Standard) is the analytical standard of Glutarylcarnitine. This product is intended for research and analytical applications. Glutarylcarnitine is the diagnostic metabolite for malonic aciduria and glutaric aciduria type I monitored in most tandem mass spectrometry newborn screening programmes.
Product Specifications
CAS Number
102636-82-8
UNSPSC
12352100
Target
Endogenous Metabolite; Reference Standards
Related Pathways
Metabolic Enzyme/Protease; Others
Field of Research
Metabolic Disease
Smiles
C[N+](C)(C)C[C@H](OC(CCCC(O)=O)=O)CC([O-])=O
Molecular Formula
C12H21NO6
Molecular Weight
275.30
References & Citations
[1]Johnson DW, et al. Stability of malonylcarnitine and Glutarylcarnitine in stored blood spots. J Inherit Metab Dis. 2004;27 (6) :789-90.|[2]S Tortorelli, et al. The urinary excretion of glutarylcarnitine is an informative tool in the biochemical diagnosis of glutaric acidemia type I. Mol Genet Metab. 2005 Feb;84 (2) :137-43.
Shipping Conditions
Room temperature
Scientific Category
Reference Standards
Frequently Asked Questions
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