Glutarylcarnitine (lithium) (Standard)

Glutarylcarnitine (lithium) (Standard) is the analytical standard of Glutarylcarnitine (lithium) . This product is intended for research and analytical applications. Glutarylcarnitine lithium is the diagnostic metabolite for malonic aciduria and glutaric aciduria type I monitored in most tandem mass spectrometry newborn screening programmes[1].

Product Specifications

UNSPSC

12352100

Target

Endogenous Metabolite; Reference Standards

Related Pathways

Metabolic Enzyme/Protease; Others

Field of Research

Metabolic Disease

Smiles

C[N+](C)(C)C[C@H](OC(CCCC(O[Li])=O)=O)CC([O-])=O

Molecular Formula

C12H20LiNO6

Molecular Weight

281.23

References & Citations

[1]Johnson DW, et al. Stability of malonylcarnitine and Glutarylcarnitine in stored blood spots. J Inherit Metab Dis. 2004;27 (6) :789-90.|[2]S Tortorelli, et al. The urinary excretion of glutarylcarnitine is an informative tool in the biochemical diagnosis of glutaric acidemia type I. Mol Genet Metab. 2005 Feb;84 (2) :137-43.