Glutarylcarnitine (lithium) (Standard)
Glutarylcarnitine (lithium) (Standard) is the analytical standard of Glutarylcarnitine (lithium) . This product is intended for research and analytical applications. Glutarylcarnitine lithium is the diagnostic metabolite for malonic aciduria and glutaric aciduria type I monitored in most tandem mass spectrometry newborn screening programmes[1].
Product Specifications
UNSPSC
12352100
Target
Endogenous Metabolite; Reference Standards
Related Pathways
Metabolic Enzyme/Protease; Others
Field of Research
Metabolic Disease
Smiles
C[N+](C)(C)C[C@H](OC(CCCC(O[Li])=O)=O)CC([O-])=O
Molecular Formula
C12H20LiNO6
Molecular Weight
281.23
References & Citations
[1]Johnson DW, et al. Stability of malonylcarnitine and Glutarylcarnitine in stored blood spots. J Inherit Metab Dis. 2004;27 (6) :789-90.|[2]S Tortorelli, et al. The urinary excretion of glutarylcarnitine is an informative tool in the biochemical diagnosis of glutaric acidemia type I. Mol Genet Metab. 2005 Feb;84 (2) :137-43.
Shipping Conditions
Room temperature
Scientific Category
Reference Standards
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