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RTC13 (Standard)

RTC13 (Standard) is the analytical standard of RTC13 (HY-101459) . This product is intended for research and analytical applications. RTC13 restores dystrophin expression and improves muscle function in the mdx mouse model for Duchenne muscular dystrophy (DMD) [1].

Product Specifications

CAS Number

[1359825-94-7]

Target

Dystrophin; Reference Standards

Related Pathways

Cytoskeleton; Others

Field of Research

Metabolic Disease

Smiles

O=[N+](C1=C(C=CC=C1)C2=CC=C(/C=C3C(NC(S/3)=N)=O)O2)[O-]

Molecular Formula

C14H9N3O4S

Molecular Weight

315.30

References & Citations

[1]Refik Kayali, et al. Read-through compound 13 restores dystrophin expression and improves muscle function in the mdx mouse model for Duchenne muscular dystrophy. Hum Mol Genet. 2012 Sep 15;21 (18) :4007-20.

Shipping Conditions

Room temperature

Scientific Category

Reference Standards

Curated Selection

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