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Glyco-3ß,5?,6ß -trihydroxycholanoic acid (NPCBA2)

Product Specifications

CAS Number

1917340-40-9

Target

Endogenous Metabolite

Related Pathways

Metabolism

Bioactivity

Glyco-3ß,5?,6ß-trihydroxycholanoic acid (NPCBA2) is a bile acid that preferentially accumulates in individuals with Niemann-Pick disease (NPC) . It serves as a biomarker for the early diagnosis of Niemann-Pick disease.

Smiles

C[C@@]12[C@@]3([C@]([C@]4([C@](C)(CC3)[C@@]([C@@H](CCC(NCC(O)=O)=O)C)(CC4)[H])[H])(C[C@@H](O)[C@@]1(O)C[C@@H](O)CC2)[H])[H]

Molecular Formula

C26H43NO6

Molecular Weight

465.62

Shipping Conditions

Cool pack

Storage Temperature

-20°C

Available Sizes

Curated Selection

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