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MMAA/cblA Polyclonal Antibody, PE-Cy5 Conjugated

Product Specifications

Background

The protein encoded by this gene is involved in the translocation of cobalamin into the mitochondrion, where it is used in the final steps of adenosylcobalamin synthesis. Adenosylcobalamin is a coenzyme required for the activity of methylmalonyl-CoA mutase. Defects in this gene are a cause of methylmalonic aciduria. [provided by RefSeq, Jul 2008].

Synonyms

Mitochondrial; cblA; MMAA protein; Methylmalonic aciduria cobalamin deficiency cblA type; Methylmalonic aciduria cobalamin deficiency type A; Methylmalonic aciduria type A protein; Methylmalonic aciduria type A protein mitochondrial; MMAA; MMAA_HUMAN.

Gene ID

166785

Host

Rabbit

Cross Reactivity

Mouse

Immunogen

21-120/418

Target

MMAA/cblA

Clonality

Polyclonal

Isotype

IgG

Conjugation

PE-Cy5

Source

KLH conjugated synthetic peptide derived from human MMAA/cblA

Applications

WB

Purification

Purified by Protein A.

Excitation Emission

488nm/670nm

Concentration

1µg/µl

Dilution

WB (1:300-5000)

Buffer

Aqueous buffered solution containing 0.01M TBS (pH7.4) with 1% BSA, 0.02% Proclin300 and 50% Glycerol.

Modification

Unmodified

Storage Conditions

Store at -20°C. Aliquot into multiple vials to avoid repeated freeze-thaw cycles.

Gene ID URL

166785

Predicted Cross Reactivity

Human, Rat

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