FH Polyclonal Antibody, Cy7 Conjugated

Product Specifications

Background

Defects in FH are the cause of fumarase deficiency (FHD) also known as fumaricaciduria. FHD is characterized by progressive encephalopathy, developmental delay, hypotonia, cerebral atrophy and lactic and pyruvic acidemia.

Synonyms

Mitochondrial; FH; Fumarase; Fumarate hydratase; Fumarate hydratase mitochondrial; FUMH_HUMAN; HLRCC; LRCC; MCL; MCUL 1; MCUL1; Multiple hereditary cutaneous leiomyomata.

Gene ID

2271

Cellular Locus

Cytoplasm

Host

Rabbit

Cross Reactivity

Mouse, Rat

Immunogen

411-510/510

Target

Clonality

Polyclonal

Isotype

IgG

Conjugation

Cy7

Source

KLH conjugated synthetic peptide derived from human Fumarate hydratase (447-496aa)

Applications

IF (IHC-P), IF (IHC-F), IF (ICC)

Purification

Purified by Protein A.

Excitation Emission

743nm/767nm

Concentration

1µg/µl

Dilution

IF (IHC-P) (1:50-200), IF (IHC-F) (1:50-200), IF (ICC) (1:50-200)

Buffer

Aqueous buffered solution containing 0.01M TBS (pH 7.4) with 1% BSA, 0.02% Proclin300 and 50% Glycerol.

Modification

Unmodified

Storage Conditions

Store at -20°C. Aliquot into multiple vials to avoid repeated freeze-thaw cycles.

Gene ID URL

2271

Predicted Cross Reactivity

Human, Dog, Cow, Sheep, Pig, Horse, Rabbit

Curated Selection

Explore Other Products

Discover premium biology products from our extensive collection of 20M+ items

NBP3-24255JF549 0.1 mL

Mouse Monoclonal MRP4/ABCC4 Antibody (ABCC4/9018) [Janelia Fluor 549]

Ask

View Details

NBP3-11675AF700 0.1 mL

Mouse Monoclonal NALP6 Antibody (Clint-1) [Alexa Fluor 700]

Ask

View Details

126978-ML405 100 µL

FRG1 (FSHD Region Gene 1 Protein, FRG1A, FSG1, Protein FRG1) (MaxLight 405) discontinued

Ask

View Details

AR09328PU-N 100 µg

ERK2 (1-360, His-tag) Human Protein

Ask

View Details

MA1102-01 50 μL

Rabbit Anti-Human Cytokeratin 7 mAb

Ask

View Details

MA1102-02 100 μL

Rabbit Anti-Human Cytokeratin 7 mAb

Ask

View Details