FH Polyclonal Antibody, AbBy Fluor™ 350 Conjugated
Product Specifications
Background
Defects in FH are the cause of fumarase deficiency (FHD) also known as fumaricaciduria. FHD is characterized by progressive encephalopathy, developmental delay, hypotonia, cerebral atrophy and lactic and pyruvic acidemia.
Synonyms
Mitochondrial; FH; Fumarase; Fumarate hydratase; Fumarate hydratase mitochondrial; FUMH_HUMAN; HLRCC; LRCC; MCL; MCUL 1; MCUL1; Multiple hereditary cutaneous leiomyomata.
Gene ID
2271
Cellular Locus
Cytoplasm
Host
Rabbit
Cross Reactivity
Mouse, Rat
Immunogen
411-510/510
Target
FH
Clonality
Polyclonal
Isotype
IgG
Conjugation
AbBy Fluor™ 350
Source
KLH conjugated synthetic peptide derived from human Fumarate hydratase (447-496aa)
Applications
IF (IHC-P), IF (IHC-F), IF (ICC)
Purification
Purified by Protein A.
Excitation Emission
346nm/442nm
Concentration
1µg/µl
Dilution
IF (IHC-P) (1:50-200), IF (IHC-F) (1:50-200), IF (ICC) (1:50-200)
Buffer
Aqueous buffered solution containing 0.01M TBS (pH7.4) with 1% BSA, 0.02% Proclin300 and 50% Glycerol.
Modification
Unmodified
Storage Conditions
Store at -20°C. Aliquot into multiple vials to avoid repeated freeze-thaw cycles.
Gene ID URL
2271
Predicted Cross Reactivity
Human, Dog, Cow, Sheep, Pig, Horse, Rabbit
Curated Selection
Explore Other Products
Discover premium biology products from our extensive collection of 20M+ items
249869-APC 100 µL
PCK1 (Phosphoenolpyruvate Carboxykinase 1 (Soluble), MGC22652, PEPCK-C, PEPCK1, PEPCKC) (APC)
Ask
View Details 
MBS2145864-01 0.1 mL
Cy3-Linked Monoclonal Antibody to Killer Cell Immunogloulin Like Receptor 2DL1 (KIR2DL1)
Ask
View Details 
MBS2145864-02 0.2 mL
Cy3-Linked Monoclonal Antibody to Killer Cell Immunogloulin Like Receptor 2DL1 (KIR2DL1)
Ask
View Details