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OPA3 Polyclonal Antibody, AbBy Fluor™ 555 Conjugated

Product Specifications

Background

OPA3 may play some role in mitochondrial processes. Defects in OPA3 are the cause of 3-methylglutaconic aciduria type 3 (MGA3), also known as optic atrophy plus syndrome, and of optic atrophy type 3 (OPA3), also known as autosomal dominant optic atrophy and cataract (ADOAC) .

Synonyms

FLJ22187; FLJ25932; Iraqi Jewish optic atrophy plus (3 methylglutaconicaciduria type 3) ; MGA3; MGC75494; OPA 3; OPA3 protein; Optic atrophy 3 (autosomal recessive, with chorea and spastic paraplegia) ; Optic atrophy 3 (Iraqi Jewish 'optic atrophy plus') ; Optic atrophy 3; Optic atrophy 3 protein.

Gene ID

80207

Swiss Prot

Q9H6K4

Cellular Locus

Cytoplasm

Host

Rabbit

Cross Reactivity

Mouse

Immunogen

1-100/179

Target

OPA3

Clonality

Polyclonal

Isotype

IgG

Conjugation

AbBy Fluor™ 555

Source

KLH conjugated synthetic peptide derived from human OPA3

Applications

IF (IHC-P), IF (IHC-F), IF (ICC)

Purification

Purified by Protein A.

Excitation Emission

553nm/568nm

Concentration

1µg/µl

Dilution

IF (IHC-P) (1:50-200), IF (IHC-F) (1:50-200), IF (ICC) (1:50-200)

Buffer

Aqueous buffered solution containing 0.01M TBS (pH7.4) with 1% BSA, 0.02% Proclin300 and 50% Glycerol.

Modification

Unmodified

Storage Conditions

Store at -20°C. Aliquot into multiple vials to avoid repeated freeze-thaw cycles.

Gene ID URL

80207

Predicted Cross Reactivity

Human, Dog, Cow, Sheep, Horse

Curated Selection

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