Miglustat HCl
Product Specifications
Background
Orally active ceramide-specific glycosyltransferase and α-glucosidase I and II inhibitor.1 Rescues trafficking-deficient F508del-CFTR in human airway epithelial cells via inhibition of ER α-glucosidases I and II.2 Pharmacological chaperone for glucocerebrosidase degradation.3 Clinically useful agent for Gaucher disease type 1.4 Stabilizes neurological disorders in Niemann-Pick disease type C.5
Conjugation
Unconjugated
Buffer
White solid
Storage Conditions
-20°C
Available Sizes
Frequently Asked Questions
More Discoveries
Explore Other Products
Browse additional items from our catalog
MBS6316218-01 0.2 mL
LIN28A, ID (LIN28A, CSDD1, LIN28, ZCCHC1, Protein lin-28 homolog A, Zinc finger CCHC domain-containing protein 1) (AP)
Sign In for Pricing
View Details MBS6316218-02 5x 0.2 mL
LIN28A, ID (LIN28A, CSDD1, LIN28, ZCCHC1, Protein lin-28 homolog A, Zinc finger CCHC domain-containing protein 1) (AP)
Sign In for Pricing
View Details