SGSH Rabbit Monoclonal Antibody
Product Specifications
Background
Cell localization:Lysosome..This gene encodes the enzyme sμLfamidase; one of several enzymes involved in the lysosomal degradation of heparan sμLfate. Mutations in this gene are associated with the lysosomal storage disease mucopolysaccaridosis IIIA, also known as Sanfilippo syndrome A, which resμLts from impaired degradation of heparan sμLfate. Transcripts of varying sizes have been reported but their biological validity has not been determined. [provided by RefSeq, Jun 2017]
Product Name Alternative
SGSH; HSS; N-sμLphoglucosamine sμLphohydrolase ; SμLfoglucosamine sμLfamidase; SμLphamidase
Gene Name
SGSH; HSS
Gene ID
6448
Swiss Prot
P51688
Host
Rabbit
Reactivity
Human
Clonality
Monoclonal
Conjugation
Unconjugated
Applications
WB, IHC, ICC/IF
Purification
Protein A
Dilution
WB 1:1000-1:5000, IHC 1:100-1:300, ICC/IF 1:100-1:300
Form
Liquid
Buffer
PBS, 50% glycerol, 0.05% Proclin 300, 0.05%BSA
Modification
Unmodified
Molecular Weight
CalcμLated MW:; Observed MW:55kD
Storage Conditions
Store at 4°C short term. Aliquot and store at -20°C for 12 months. Avoid freeze/thaw cycles.
Isotype
IgG, Kappa
Available Sizes
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