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UPB1 Rabbit Monoclonal Antibody

Product Specifications

Background

Cell localization:Cytoplasm..This gene encodes a protein that belongs to the CN hydrolase family. Beta-ureidopropionase catalyzes the last step in the pyrimidine degradation pathway. The pyrimidine bases uracil and thymine are degraded via the consecutive action of dihydropyrimidine dehydrogenase (DHPDH), dihydropyrimidinase (DHP) and beta-ureidopropionase (UP) to beta-alanine and beta-aminoisobutyric acid, respectively. UP deficiencies are associated with N-carbamyl-beta-amino aciduria and may lead to abnormalities in neurological activity. [provided by RefSeq, JμL 2008]

Product Name Alternative

UPB1; BUP1; Beta-ureidopropionase ; BUP-1; Beta-alanine synthase; N-carbamoyl-beta-alanine amidohydrolase

Gene Name

UPB1; BUP1

Gene ID

51733

Swiss Prot

Q9UBR1

Host

Rabbit

Reactivity

Human

Clonality

Monoclonal

Conjugation

Unconjugated

Applications

WB, IHC, IP

Purification

Protein A

Dilution

WB 1:1000-1:5000, IHC 1:100-1:300, IP 1:50-1:100

Form

Liquid

Buffer

PBS, 50% glycerol, 0.05% Proclin 300, 0.05%BSA

Modification

Unmodified

Molecular Weight

CalcμLated MW:; Observed MW:42kD

Storage Conditions

Store at 4°C short term. Aliquot and store at -20°C for 12 months. Avoid freeze/thaw cycles.

Isotype

IgG, Kappa

Available Sizes

Frequently Asked Questions

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