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Galactosidase alpha Rabbit Monoclonal antibody

Product Specifications

Background

Defects in GLA are the cause of Fabry disease (FD) [MIM:301500]. FD is a rare X-linked sphingolipidosis disease where glycolipid accumulates in many tissues. The disease consists of an inborn error of glycosphingolipid catabolism.

Product Name Alternative

Alpha gal A; GALA; Galactosidase; alpha; GLA; Melibiase

Gene Name

GLA

Gene ID

2717

Swiss Prot

P06280

Host

Rabbit

Reactivity

Human

Clonality

Monoclonal

Conjugation

Unconjugated

Applications

WB, IHC, IP

Field of Research

Cardiovascular

Purification

Affinity Purified

Dilution

WB 1:500-1:1000, IHC 1:50-1:100, IP 1:20-1:50

Form

Liquid

Buffer

50mM Tris-Glycine (pH 7.4), 0.15M NaCl, 40% Glycerol, 0.01% Sodium azide and 0.05% BSA

Modification

Unmodified

Molecular Weight

Calculated MW: 49 kDa; Observed MW: 49 kDa

Storage Conditions

Store at 4°C short term. Aliquot and store at -20°C for 12 months. Avoid freeze/thaw cycles.

Isotype

IgG

Available Sizes

Curated Selection

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