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DL-3-AMINOISOBUTYRIC ACID

Beta-aminoisobutyric acid is the product from the conversion of N-carbamyl-beta-aminoisobutyric acid by the enzyme Beta-ureidopropionase (EC 3.5.1.6) the last step in pyrimidine degradation. Beta-ureidopropionase deficiency is an inborn error of pyrimidine degradation associated with neurological abnormalities.

Product Specifications

CAS Number

144-90-1

Stability

≥ 2 years

Purity

>98% (HPLC)

Weight

103.12

Molecular Formula

C4H9NO2

Notes

Research use only, not for human use.

Receptor

Human Endogenous Metabolite

Available Sizes

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