4-Methylumbelliferyl-α- L-iduronic acid cyclohexylammonium salt

4-Methylumbelliferyl-α- L-iduronic acid cyclohexylammonium salt is a fluorogenic soluble enzyme substrate for α-L-iduronidase. α-L-iduronidase is deficient in the genetic disorder Mucopolysaccharidosis type I, also called Hurler syndrome. 4-Methylumbelliferyl-α-L-iduronide is used in the diagnosis of Hurler syndrome as the substrate in an enzymatic assay of α-L-iduronidase activity.Product Specifications4-Methylumbelliferyl-α- L-iduronic acid cyclohexylammonium salt4-Methylumbelliferyl-α-L-iduronide.4-MU-α-L-IdoA • CHXMOLECULAR BIOLOGY GRADEFormula: C16H16O9· C6H13NMW: 451.48 g/mol