4-Methylumbelliferyl a-L-idopyranosiduronic acid sodium salt

4-Methylumbelliferyl alpha-L-idopyranosiduronic acid sodium salt is a carbohydrate acid and organic sodium salt applied as an indicator. It is the fluorogenic substrate used in assays of α-L-Iduronidase and iduronate-2-sulfatase for identifying Hurler syndrome, also called mucopolysaccharidosis type I (MPS I) . The disorder is characterized by α -L iduronidase enzyme deficiency, resulting in the buildup of glucosaminoglycans. Tests measure the chemical products 4-MU-α-IdoA or fluorophate 4-MU emitted following the enzymatic action of 4-Methylumbelliferyl alpha-L-idopyranosiduronic acid sodium salt. The substance is a white crystalline powder and is soluble in ethanol, methanol and water.Product Specifications4-Methylumbelliferyl alpha-L-idopyranosiduronic acid sodium salt4-Methylumbelliferyl a-L-iduronicacid sodium saltSodium 4-methyl-2-oxo-2H-chromen-7-yl α-L-idopyranosiduronateSodium (4-methylumbelliferyla-L-idopyranosid) urinateFormula:C16H15NaO9MW:374.27 g/mol