Recombinant PDHA1 Monoclonal Antibody
Product Specifications
Background
PDHA1, also named as PHE1A, is one of the 3 enzymes of the pyruvate dehydrogenase complex. It is a nuclear-encoded mitochondrial matrix multienzyme complex that provides the primary link between glycolysis and the tricarboxylic acid (TCA) cycle by catalyzing the irreversible conversion of pyruvate into acetyl-CoA. Defects in PDHA1 are a cause of pyruvate dehydrogenase E1-alpha deficiency (PDHAD) and X-linked Leigh syndrome (X-LS) .
Abbreviation
PDHA1
UniProt
P08559
Host
Rabbit
Reactivity
Human; Rat; Mouse
Immunogen
Recombinant human PDHA1 fragment
Target
PDHA1; PDHA; PDHAD; PDHCE1A; PHE1A; E1 alpha polypeptide 1; mitochondrial; ODPA; PDH; PDHE1 A type I; PDHE1-A type I; PDHα; Pyruvate Dehydrogenase (lipoamide) alpha 1; Pyruvate dehydrogenase complex; Pyruvate Dehydrogenase E1 alpha; Pyruvate dehydrogenase E1 component subunit alpha; somatic form
Clonality
Monoclonal,Recombinant
Clone
A520
Conjugation
Unconjugated
Applications
WB
Field of Research
Signal Transduction; Cancer; Metabolism
Purification
Protein A purified
Concentration
1 mg/mL
Dilution
WB 1:500-1:1000
Buffer
PBS, 50% glycerol, 0.05% Proclin 300, 0.05% protein protectant.
Shipping Conditions
Ice bag
Storage Conditions
Store at -20°C Valid for 12 months. Avoid freeze / thaw cycles.
Calculated Molecular Weight
43 kDa
Observed Molecular Weight
43 kDa
Isotype
IgG, κ
Available Sizes
Curated Selection
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