GNS Antibody
Product Specifications
Background
GNS is a lysosomal enzyme found in all cells. It is involved in the catabolism of heparin, heparan sulphate, and keratan sulphate. Deficiency of this enzyme results in the accumulation of undegraded substrate and the lysosomal storage disorder mucopolysaccharidosis type IIID (Sanfilippo D syndrome) . Mucopolysaccharidosis type IIID is the least common of the four subtypes of Sanfilippo syndrome.
NCBI Gene ID
2799
Swiss Prot
P15586
Accession Number
P15586
Host
Rabbit
Reactivity
Human
Immunogen
This GNS antibody is generated from rabbits immunized with a KLH conjugated synthetic peptide between 283-313 amino acids from the Central region of human GNS.
Clonality
Polyclonal
Conjugation
Unconjugated
Type
Primary Antibodies
Field of Research
Cell Cycle, Obesity, Signal Transduction
Purification
This antibody is prepared by Saturated Ammonium Sulfate (SAS) precipitation followed by dialysis
Concentration
Batch dependent
Buffer
Supplied in PBS with 0.09% (W/V) sodium azide.
Modification
None
Shipping Conditions
Blue Ice
Storage Conditions
Store at 4˚ C for three months and -20˚ C, stable for up to one year. As with all antibodies care should be taken to avoid repeated freeze thaw cycles. Antibodies should not be exposed to prolonged high temperatures.
Product Datasheet
https://www.prosci-inc.com/?datasheet_sku=62-334
Calculated Molecular Weight
62 kDa
Fragment
Rabbit Ig
Symbol
GNS
NCBI Official Name
N-acetylglucosamine-6-sulfatase
NCBI Organism
Homo sapiens
Background Reference 01
Zhang, H., Li, X.J., Nat. Biotechnol. 21 (6), 660-666 (2003)
Other Product Names
N-acetylglucosamine-6-sulfatase, Glucosamine-6-sulfatase, G6S, GNS
Tested Applications
WB, IHC-P, Flow
Protein ID
232126
Physical Properties
Liquid
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