What is the catalog number for GAA Antibody?

The catalog number for GAA Antibody is 56-495.

What sizes are available for GAA Antibody?

GAA Antibody is available in the following size(s): 400 µL.

Is GAA Antibody in stock?

GAA Antibody is currently made to order / not held in immediate stock. Contact us for lead time.

GAA Antibody

Product Specifications

Background

This gene encodes acid alpha-glucosidase, which is essential for the degradation of glycogen to glucose in lysosomes. Different forms of acid alpha-glucosidase are obtained by proteolytic processing. Defects in this gene are the cause of glycogen storage disease II, also known as Pompe's disease, which is an autosomal recessive disorder with a broad clinical spectrum. Three transcript variants encoding the same protein have been found for this gene.

NCBI Gene ID

2548

Swiss Prot

P10253

Accession Number

P10253

Host

Rabbit

Reactivity

Human

Immunogen

This GAA antibody is generated from rabbits immunized with a KLH conjugated synthetic peptide between 174-203 amino acids from the N-terminal region of human GAA.

Clonality

Polyclonal

Conjugation

Unconjugated

Type

Primary Antibodies

Field of Research

Obesity, Signal Transduction

Purification

This antibody is purified through a protein A column, followed by peptide affinity purification.

Concentration

Batch dependent

Buffer

Supplied in PBS with 0.09% (W/V) sodium azide.

Modification

None

Shipping Conditions

Blue Ice

Storage Conditions

Store at 4˚ C for three months and -20˚ C, stable for up to one year. As with all antibodies care should be taken to avoid repeated freeze thaw cycles. Antibodies should not be exposed to prolonged high temperatures.