SGSH Antibody
Product Specifications
Background
This gene encodes one of several enzymes involved in the lysosomal degradation of heparan sulfate. Mutations in this gene are associated with Sanfilippo syndrome A, one type of the lysosomal storage disease mucopolysaccaridosis III, which results from impaired degradation of heparan sulfate. Transcripts of varying sizes have been reported but their biological validity has not been determined.
NCBI Gene ID
6448
Swiss Prot
P51688
Host
Rabbit
Reactivity
Human, Mouse, Rat
Immunogen
Recombinant fusion protein containing a sequence corresponding to amino acids 273-502 of human SGSH (NP_000190.1) .
Clonality
Polyclonal
Conjugation
Unconjugated
Type
Primary Antibodies
Field of Research
Cell Cycle, Neuroscience, Signal Transduction
Purification
Affinity purification
Positive Control
MCF7
Concentration
Batch dependent
Buffer
PBS with 0.02% sodium azide, 50% glycerol, pH7.3.
Modification
None
Shipping Conditions
Blue Ice
Storage Conditions
Store at -20˚ C. Avoid freeze / thaw cycles.
Calculated Molecular Weight
Observed: 63kDa
Fragment
IgG
Symbol
SGSH
Positive Control 2
22Rv1
Positive Control 3
HepG2
Positive Control 4
Mouse liver
Positive Control 5
Mouse testis
NCBI Official Name
N-sulphoglucosamine sulphohydrolase
NCBI Organism
Homo sapiens
Other Product Names
N-sulphoglucosamine sulphohydrolase, Sulfoglucosamine sulfamidase, Sulphamidase, SGSH, HSS
Tested Applications
WB, IHC
Physical Properties
Liquid
Curated Selection
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