CTNS Antibody
Product Specifications
Background
This gene encodes a seven-transmembrane domain protein that functions to transport cystine out of lysosomes. Its activity is driven by the H+ electrochemical gradient of the lysosomal membrane. Mutations in this gene cause cystinosis, a lysosomal storage disorder. Alternative splicing results in multiple transcript variants.
NCBI Gene ID
1497
Swiss Prot
O60931
Host
Rabbit
Reactivity
Human, Mouse, Rat
Immunogen
Recombinant fusion protein containing a sequence corresponding to amino acids 1-120 of human CTNS (NP_001026851.2) .
Clonality
Polyclonal
Conjugation
Unconjugated
Type
Primary Antibodies
Field of Research
Signal Transduction
Purification
Affinity purification
Positive Control
HeLa
Concentration
Batch dependent
Buffer
PBS with 0.02% sodium azide, 50% glycerol, pH7.3.
Modification
None
Shipping Conditions
Blue Ice
Storage Conditions
Store at -20˚ C. Avoid freeze / thaw cycles.
Calculated Molecular Weight
Observed: 42kDa
Fragment
IgG
Symbol
CTNS
Positive Control 2
SW480
Positive Control 3
HepG2
Positive Control 4
293T
Positive Control 5
Mouse kidney
Positive Control 6
Mouse skeletal muscle
NCBI Official Name
Cystinosin, lysosomal cystine transporter
NCBI Organism
Homo sapiens
Other Product Names
CTNS, Cystinosin, Cystinosis, nephropathic, CTNS-LSB, PQLC4
Tested Applications
WB, IF
Physical Properties
Liquid
Curated Selection
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