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CLN3 Antibody

Product Specifications

Background

This gene encodes a protein that is involved in lysosomal function. Mutations in this, as well as other neuronal ceroid-lipofuscinosis (CLN) genes, cause neurodegenerative diseases commonly known as Batten disease or collectively known as neuronal ceroid lipofuscinoses (NCLs) . Many alternatively spliced transcript variants have been found for this gene.

NCBI Gene ID

1201

Swiss Prot

Q13286

Host

Rabbit

Reactivity

Human, Mouse, Rat

Immunogen

Recombinant fusion protein containing a sequence corresponding to amino acids 1-280 of human CLN3 (NP_001035897.1) .

Clonality

Polyclonal

Conjugation

Unconjugated

Type

Primary Antibodies

Field of Research

Apoptosis, Cell Cycle, Neuroscience

Purification

Affinity purification

Positive Control

Mouse liver

Concentration

Batch dependent

Buffer

PBS with 0.02% sodium azide, 50% glycerol, pH7.3.

Modification

None

Shipping Conditions

Blue Ice

Storage Conditions

Store at -20˚ C. Avoid freeze / thaw cycles.

Calculated Molecular Weight

Observed: 48kDa

Fragment

IgG

Symbol

CLN3

Positive Control 2

Rat liver

NCBI Official Name

CLN3 lysosomal/endosomal transmembrane protein, battenin

NCBI Organism

Homo sapiens

Other Product Names

BTN1, BTS, JNCL, battenin, CLN3, battenin, batten disease protein, ceroid-lipofuscinosis, neuronal 3

Tested Applications

WB, IHC

Physical Properties

Liquid

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