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PAH Antibody

Product Specifications

Background

PAH encodes the enzyme phenylalanine hydroxylase that is the rate-limiting step in phenylalanine catabolism. Deficiency of this enzyme activity results in the autosomal recessive disorder phenylketonuria.

NCBI Gene ID

5053

Swiss Prot

P00439

Host

Rabbit

Reactivity

Human, Mouse, Rat

Immunogen

Recombinant fusion protein containing a sequence corresponding to amino acids 1-290 of human PAH (NP_000268.1) .

Clonality

Polyclonal

Conjugation

Unconjugated

Type

Primary Antibodies

Field of Research

Signal Transduction

Purification

Affinity purification

Positive Control

U-251MG

Concentration

Batch dependent

Buffer

PBS with 0.02% sodium azide, 50% glycerol, pH7.3.

Modification

None

Shipping Conditions

Blue Ice

Storage Conditions

Store at -20˚ C. Avoid freeze / thaw cycles.

Calculated Molecular Weight

Observed: 55kDa

Fragment

IgG

Applications Notes

WB: 1:500 - 1:2000

Symbol

PAH

Positive Control 2

HepG2

Positive Control 3

Mouse liver

Positive Control 4

Mouse kidney

NCBI Official Name

Phenylalanine hydroxylase

NCBI Organism

Homo sapiens

Other Product Names

PAH, PKU1, PKU, phenylalanine hydroxylase, PH

Tested Applications

WB

Physical Properties

Liquid

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