PAH Antibody
Product Specifications
Background
PAH encodes the enzyme phenylalanine hydroxylase that is the rate-limiting step in phenylalanine catabolism. Deficiency of this enzyme activity results in the autosomal recessive disorder phenylketonuria.
NCBI Gene ID
5053
Swiss Prot
P00439
Host
Rabbit
Reactivity
Human, Mouse, Rat
Immunogen
Recombinant fusion protein containing a sequence corresponding to amino acids 1-290 of human PAH (NP_000268.1) .
Clonality
Polyclonal
Conjugation
Unconjugated
Type
Primary Antibodies
Field of Research
Signal Transduction
Purification
Affinity purification
Positive Control
U-251MG
Concentration
Batch dependent
Buffer
PBS with 0.02% sodium azide, 50% glycerol, pH7.3.
Modification
None
Shipping Conditions
Blue Ice
Storage Conditions
Store at -20˚ C. Avoid freeze / thaw cycles.
Calculated Molecular Weight
Observed: 55kDa
Fragment
IgG
Applications Notes
WB: 1:500 - 1:2000
Symbol
PAH
Positive Control 2
HepG2
Positive Control 3
Mouse liver
Positive Control 4
Mouse kidney
NCBI Official Name
Phenylalanine hydroxylase
NCBI Organism
Homo sapiens
Other Product Names
PAH, PKU1, PKU, phenylalanine hydroxylase, PH
Tested Applications
WB
Physical Properties
Liquid
Curated Selection
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