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FUCA1 Antibody

Product Specifications

Background

The protein encoded by this gene is a lysosomal enzyme involved in the degradation of fucose-containing glycoproteins and glycolipids. Mutations in this gene are associated with fucosidosis (FUCA1D), which is an autosomal recessive lysosomal storage disease. A pseudogene of this locus is present on chr 2.

NCBI Gene ID

2517

Swiss Prot

P04066

Host

Rabbit

Reactivity

Human, Mouse, Rat

Immunogen

Recombinant fusion protein containing a sequence corresponding to amino acids 253-395 of human FUCA1 (NP_000138.2) .

Clonality

Polyclonal

Conjugation

Unconjugated

Type

Primary Antibodies

Field of Research

Cancer, Signal Transduction

Purification

Affinity purification

Positive Control

Mouse kidney

Concentration

Batch dependent

Buffer

PBS with 0.02% sodium azide, 50% glycerol, pH7.3.

Modification

None

Shipping Conditions

Blue Ice

Storage Conditions

Store at -20˚ C. Avoid freeze / thaw cycles.

Calculated Molecular Weight

Observed: 53kDa

Fragment

IgG

Applications Notes

WB: 1:500 - 1:2000

Symbol

FUCA1

Positive Control 2

Rat liver

NCBI Official Name

Fucosidase, alpha-L- 1, tissue

NCBI Organism

Homo sapiens

Other Product Names

FUCA1, FUCA

Tested Applications

WB

Physical Properties

Liquid

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