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FAH Antibody

Product Specifications

Background

This gene encodes the last enzyme in the tyrosine catabolism pathway. FAH deficiency is associated with Type 1 hereditary tyrosinemia (HT) .

NCBI Gene ID

2184

Swiss Prot

P16930

Host

Rabbit

Reactivity

Human, Mouse, Rat

Immunogen

Recombinant fusion protein containing a sequence corresponding to amino acids 1-419 of human FAH (NP_000128.1) .

Clonality

Polyclonal

Conjugation

Unconjugated

Type

Primary Antibodies

Field of Research

Cancer, Signal Transduction

Purification

Affinity purification

Positive Control

Mouse liver

Concentration

Batch dependent

Buffer

PBS with 0.02% sodium azide, 50% glycerol, pH7.3.

Modification

None

Shipping Conditions

Blue Ice

Storage Conditions

Store at -20˚ C. Avoid freeze / thaw cycles.

Calculated Molecular Weight

Observed: 46kDa

Fragment

IgG

Symbol

FAH

Positive Control 2

Mouse kidney

Positive Control 3

Rat liver

Positive Control 4

Rat kidney

NCBI Official Name

Fumarylacetoacetate hydrolase (fumarylacetoacetase)

NCBI Organism

Homo sapiens

Other Product Names

FAH

Tested Applications

WB, IHC

Physical Properties

Liquid

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