FKRP Antibody
Product Specifications
Background
This gene encodes a protein which is targeted to the medial Golgi apparatus and is necessary for posttranslational modification of dystroglycan. Mutations in this gene have been associated with congenital muscular dystrophy, mental retardation, and cerebellar cysts. Several alternatively spliced transcript variants of this gene have been described, but the full-length nature of some of these variants has not been determined.
NCBI Gene ID
79147
Swiss Prot
Q9H9S5
Host
Rabbit
Reactivity
Human, Mouse, Rat
Immunogen
Recombinant fusion protein containing a sequence corresponding to amino acids 30-220 of human FKRP (NP_077277.1) .
Clonality
Polyclonal
Conjugation
Unconjugated
Type
Primary Antibodies
Field of Research
Signal Transduction
Purification
Affinity purification
Positive Control
U-87MG
Concentration
Batch dependent
Buffer
PBS with 0.02% sodium azide, 50% glycerol, pH7.3.
Modification
None
Shipping Conditions
Blue Ice
Storage Conditions
Store at -20˚ C. Avoid freeze / thaw cycles.
Product Datasheet
https://www.prosci-inc.com/?datasheet_sku=13-491
Calculated Molecular Weight
Observed: 45kDa
Fragment
IgG
Symbol
FKRP
Positive Control 2
LO2
Positive Control 3
A-549
Positive Control 4
HT-29
Positive Control 5
293T
NCBI Official Name
Fukutin-related protein
NCBI Organism
Homo sapiens
Other Product Names
Fukutin-related protein, 2---, FKRP
Tested Applications
WB, IHC
Physical Properties
Liquid
Curated Selection
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