BBOX1 Mouse Monoclonal Antibody [Clone ID: UMLBI119]

Product Specifications

Background

This gene encodes gamma butyrobetaine hydroxylase which catalyzes the formation of L-carnitine from gamma-butyrobetaine, the last step in the L-carnitine biosynthetic pathway. Carnitine is essential for the transport of activated fatty acids across the mitochondrial membrane during mitochondrial beta-oxidation. [provided by RefSeq, Jul 2008]

Overview

Carrier-free (BSA/glycerol-free) BBOX1 mouse monoclonal antibody, clone UMLBI119

Synonyms

BBH; BBOX; G-BBH; gamma-BBH

Gene Name

Homo sapiens gamma-butyrobetaine hydroxylase 1 (BBOX1), transcript variant 1, mRNA.

Gene ID

8424

UniProt

O75936

Conjugation

Unconjugated

Related Pathways

Lysine degradation

Field of Research

Lysine degradation

Dilution

IHC 1:100~200

Form

Lyophilized powder (original buffer 1X PBS, pH 7.3, 8% trehalose)

Buffer

Lyophilized powder (original buffer 1X PBS, pH 7.3, 8% trehalose)

Storage Conditions

Stable for 1 year at -20°C from date of shipment. For maximum recovery of product, centrifuge the original vial after thawing and opening the cap. Aliquot will be stable at 4°C short term. For long-term storage, aliquot and store at -20°C or below. Stable for 12 months at -20°C. Avoid repeated freeze-thaw cycles.