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OPA3 Mouse Monoclonal Antibody [Clone ID: LBI1G3]

Product Specifications

Background

The mouse ortholog of this protein co-purifies with the mitochondrial inner membrane. Mutations in this gene have been shown to result in 3-methylglutaconic aciduria type III and autosomal dominant optic atrophy and cataract. Multiple transcript variants encoding different isoforms have been found for this gene. [provided by RefSeq, Oct 2009]

Synonyms

MGA3

Gene Name

Optic atrophy 3 (autosomal recessive, with chorea and spastic paraplegia)

Gene ID

80207

UniProt

Q9H6K4

Conjugation

Unconjugated

Concentration

1 mg/ml

Dilution

IHC 1:150

Form

PBS (PH 7.3) containing 1% BSA, 50% glycerol and 0.02% sodium azide.

Buffer

PBS (PH 7.3) containing 1% BSA, 50% glycerol and 0.02% sodium azide.

Storage Conditions

Store at +4°C short term. For long-term storage, aliquot and store at -20°C or below. Stable for 12 months at -20°C. Avoid repeated freeze-thaw cycles.

Symbol

OPA3

Overview

OPA3 mouse monoclonal antibody, clone LBI1G3

Gene ID URL

https://www.ncbi.nlm.nih.gov/gene/?term=80207

Uniprot URL

https://www.uniprot.org/uniprot/Q9H6K4

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