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Filensin (BFSP1) Mouse Monoclonal Antibody [Clone ID: LBI2B2]

Product Specifications

Background

This gene encodes a lens-specific intermediate filament-like protein named filensin. The encoded protein is expressed in lens fiber cells after differentiation has begun. This protein functions as a component of the beaded filament which is a cytoskeletal structure found in lens fiber cells. Mutations in this gene are the cause of autosomal recessive cortical juvenile-onset cataract. Alternate splicing results in multiple transcript variants. [provided by RefSeq, Jul 2013]

Overview

BFSP1 mouse monoclonal antibody, clone LBI2B2

Synonyms

CP94; CP115; CTRCT33; LIFL-H

Gene Name

Beaded filament structural protein 1

Gene ID

631

UniProt

Q12934

Conjugation

Unconjugated

Concentration

1 mg/ml

Dilution

WB 1:2000

Form

PBS (PH 7.3) containing 1% BSA, 50% glycerol and 0.02% sodium azide.

Buffer

PBS (PH 7.3) containing 1% BSA, 50% glycerol and 0.02% sodium azide.

Storage Conditions

Store at +4°C short term. For long-term storage, aliquot and store at -20°C or below. Stable for 12 months at -20°C. Avoid repeated freeze-thaw cycles.

Symbol

BFSP1

Gene ID URL

https://www.ncbi.nlm.nih.gov/gene/?term=631

Uniprot URL

https://www.uniprot.org/uniprot/Q12934

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