SPG7 Mouse Monoclonal Antibody [Clone ID: LBI5H7]

Product Specifications

Background

This gene encodes a nuclear-encoded mitochondrial metalloprotease protein that is a member of the AAA (ATPases associated with a variety of cellular activities) protein family. Members of this protein family share an ATPase domain and have roles in diverse cellular processes including membrane trafficking, intracellular motility, organelle biogenesis, protein folding, and proteolysis. Two transcript variants encoding distinct isoforms have been identified for this gene. Mutations associated with this gene cause autosomal recessive spastic paraplegia 7. [provided by RefSeq]

Overview

SPG7 mouse monoclonal antibody, clone LBI5H7

Synonyms

CAR; CMAR; PGN; SPG5C

Gene Name

SPG7, paraplegin matrix AAA peptidase subunit

Gene ID

6687

UniProt

Q9UQ90

Conjugation

Unconjugated

Concentration

1 mg/ml

Dilution

WB 1:2000, IF 1:100

Form

PBS (PH 7.3) containing 1% BSA, 50% glycerol and 0.02% sodium azide.

Buffer

PBS (PH 7.3) containing 1% BSA, 50% glycerol and 0.02% sodium azide.

Function

Protease, Transmembrane

Storage Conditions

Store at +4°C short term. For long-term storage, aliquot and store at -20°C or below. Stable for 12 months at -20°C. Avoid repeated freeze-thaw cycles.