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SPR Mouse Monoclonal Antibody [Clone ID: LBI2F7]

Product Specifications

Background

This gene encodes an aldo-keto reductase that catalyzes the NADPH-dependent reduction of pteridine derivatives and is important in the biosynthesis of tetrahydrobiopterin (BH4) . Mutations in this gene result in DOPA-responsive dystonia due to sepiaterin reductase deficiency. A pseudogene has been identified on chromosome 1. [provided by RefSeq]

Synonyms

SDR38C1

Gene Name

Sepiapterin reductase

Gene ID

6697

UniProt

P35270

Conjugation

Unconjugated

Related Pathways

Folate biosynthesis, Metabolic pathways

Field of Research

Folate biosynthesis, Metabolic pathways

Concentration

1 mg/ml

Dilution

WB 1:500~2000

Form

PBS (PH 7.3) containing 1% BSA, 50% glycerol and 0.02% sodium azide.

Buffer

PBS (PH 7.3) containing 1% BSA, 50% glycerol and 0.02% sodium azide.

Function

Druggable Genome

Storage Conditions

Store at +4°C short term. For long-term storage, aliquot and store at -20°C or below. Stable for 12 months at -20°C. Avoid repeated freeze-thaw cycles.

Symbol

SPR

Overview

SPR mouse monoclonal antibody, clone LBI2F7

Gene ID URL

https://www.ncbi.nlm.nih.gov/gene/?term=6697

Uniprot URL

https://www.uniprot.org/uniprot/P35270

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