HIBCH Mouse Monoclonal Antibody [Clone ID: LBI3D11]
Product Specifications
Background
This gene encodes the enzyme responsible for hydrolysis of both HIBYL-CoA and beta-hydroxypropionyl-CoA. Mutations in this gene have been associated with 3-hyroxyisobutyryl-CoA hydrolase deficiency. Alternative splicing results in multiple transcript variants.
Synonyms
HIBYLCOAH
Gene Name
3-hydroxyisobutyryl-CoA hydrolase
Gene ID
26275
UniProt
Q6NVY1
Conjugation
Unconjugated
Related Pathways
Beta-Alanine metabolism, Metabolic pathways, Propanoate metabolism, Valine, leucine and isoleucine degradation
Field of Research
Beta-Alanine metabolism, Metabolic pathways, Propanoate metabolism, Valine, leucine and isoleucine degradation
Concentration
0.24 mg/ml
Dilution
WB 1:500~2000, IF 1:100, FLOW 1:100
Form
PBS (PH 7.3) containing 1% BSA, 50% glycerol and 0.02% sodium azide.
Buffer
PBS (PH 7.3) containing 1% BSA, 50% glycerol and 0.02% sodium azide.
Storage Conditions
Store at +4°C short term. For long-term storage, aliquot and store at -20°C or below. Stable for 12 months at -20°C. Avoid repeated freeze-thaw cycles.
Symbol
HIBCH
Overview
Anti-HIBCH mouse monoclonal antibody, clone LBI3D11
Gene ID URL
https://www.ncbi.nlm.nih.gov/gene/?term=26275
Uniprot URL
https://www.uniprot.org/uniprot/Q6NVY1
Curated Selection
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