HIBCH Mouse Monoclonal Antibody [Clone ID: LBI3D11]

Product Specifications

Background

This gene encodes the enzyme responsible for hydrolysis of both HIBYL-CoA and beta-hydroxypropionyl-CoA. Mutations in this gene have been associated with 3-hyroxyisobutyryl-CoA hydrolase deficiency. Alternative splicing results in multiple transcript variants.

Overview

Anti-HIBCH mouse monoclonal antibody, clone LBI3D11

Synonyms

HIBYLCOAH

Gene Name

3-hydroxyisobutyryl-CoA hydrolase

Gene ID

26275

UniProt

Q6NVY1

Conjugation

Unconjugated

Related Pathways

Beta-Alanine metabolism, Metabolic pathways, Propanoate metabolism, Valine, leucine and isoleucine degradation

Field of Research

Beta-Alanine metabolism, Metabolic pathways, Propanoate metabolism, Valine, leucine and isoleucine degradation

Concentration

0.24 mg/ml

Dilution

WB 1:500~2000, IF 1:100, FLOW 1:100

Form

PBS (PH 7.3) containing 1% BSA, 50% glycerol and 0.02% sodium azide.

Buffer

PBS (PH 7.3) containing 1% BSA, 50% glycerol and 0.02% sodium azide.

Storage Conditions

Store at +4°C short term. For long-term storage, aliquot and store at -20°C or below. Stable for 12 months at -20°C. Avoid repeated freeze-thaw cycles.